A Case of Peeling Skin Syndrome
نویسندگان
چکیده
Peeling skin syndrome is a very rare autosomal recessive disease characterized by widespread painless peeling of the skin in superficial sheets. Etiology is still unknown with an autosomal recessive inheritance. Less than 100 cases have been reported in the medical literature. We present a 32-year-old man having asymptomatic peeling of skin since birth. Sheets of skin were peeling from his neck, trunk, and extremities, following friction or rubbing especially if pre-soaked in water but sparing palm and soles. Histologically, there was epidermal separation at the level of stratum corneum, just above the stratum granulosum. This case is being presented due to its rarity.
منابع مشابه
Generalized Form of Peeling Skin Syndrome: A Case Report
Peeling skin syndrome (PSS) is a very rare keratinization disorder, characterized by spontaneous exfoliation of the stratum corneum. Herein, we report a case of non-inflammatory (type A) PSS.
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Observations: Peeling skin syndrome is a very rare autosomal recessive disease characterized by widespread painless peeling of the skin in superficial sheets. We present a 31-year-old man with a lifelong history of continuous, spontaneous, asymptomatic generalized peeling skin. Histologically, there was epidermal separation at the level of stratum corneum, just above the stratum granulosum. The...
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